A Case Report of Vogt's Limbal Girdle and Retinitis Pigmentosa in a Thirteen-Year-Old Boy: A Rare and Unusual Association

نویسندگان

  • A.P. Vignesh
  • Renuka Srinivasan
  • Swathi Karanth
  • Sai Vijitha
چکیده

AIM To describe a rare case of Vogt's limbal girdle in a boy with retinitis pigmentosa. METHODS A 13-year-old boy from India presented to us with progressive diminution of vision and nyctalopia for 5 years. On examination, he had the characteristic features of retinitis pigmentosa with the fundus showing disc pallor, bony spicules and arteriolar attenuation. His anterior segment examination showed Vogt's limbal girdle in both eyes. RESULTS Vogt's limbal girdle is a corneal degeneration usually seen in elderly individuals. This is the first time it is seen in association with retinitis pigmentosa. It has also never been reported at such a young age. CONCLUSION We report a rare case where Vogt's limbal girdle was observed in a 13-year-old boy with retinitis pigmentosa. This gives further insight into the pathogenesis of the disease.

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عنوان ژورنال:

دوره 6  شماره 

صفحات  -

تاریخ انتشار 2015